선천성 무통 무한증 환자의 치과적 관리 증례보고
Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report
배철현, 이대우, 김재곤, 양연미,
소속 상세정보
배철현 ( Bae Cheol-Hyeon ) - Jeonbuk National University Dental Hospital Department of Pediatric Dentistry
이대우 ( Lee Dae-Woo ) - Jeonbuk National University Dental Hospital Department of Pediatric Dentistry
김재곤 ( Kim Jae-Gon ) - Jeonbuk National University Dental Hospital Department of Pediatric Dentistry
양연미 ( Yang Yeon-Mi ) - Jeonbuk National University Dental Hospital Department of Pediatric Dentistry
Abstract
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disorder; affected patients are characterized by inability to feel pain and to sweat over the entire body, as well as by mental retardation. Because, in the oral examination, no specific findings on soft or hard tissue may be found except possible lesions due to selfmutilation, early recognition and diagnosis are essential for these patients. Pediatric dentists must be aware of the clinical manifestations and treatment considerations related to uncontrolled body temperature, tactile hyperesthesia and lack of pain reflex. In this case report, dental management of CIPA was suggested by presenting a 6-year follow-up of young patient.
키워드
CIPA; Pain insensitivity; Anhidrosis; Self-mutilation
원문 및 링크아웃 정보
등재저널 정보